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Nodding syndrome (NS) is a poorly understood condition, which was delineated in 2008 as a new epilepsy syndrome. So far, confirmed cases of NS have been observed in three circumscribed African areas: southern Tanzania, southern Sudan, and northern Uganda. Case–control studies have provided evidence of an association between NS and infection with Onchocerca volvulus, but the causation of NS is still not fully clarified. We report a case of a 15-year old boy with head nodding seizures and other characteristic features of NS from an onchocerciasis endemic area in western Uganda, with no contiguity to the hitherto known areas. We suggest that the existence of NS should be systematically investigated in other areas.
Authors' addresses: Christoph Kaiser, Practice for Child and Adolescent Health, Baden-Baden, Germany, E-mail: firstname.lastname@example.org. Tom Rubaale and George Asaba, District Health Department, Kabarole District Local Government, Fort Portal, Uganda, E-mails: email@example.com and firstname.lastname@example.org. Ephraim Tukesiga, Vector Control Unit, Ministry of Health, Fort Portal, Uganda, E-mail: email@example.com. Walter Kipp, Department of Public Health Sciences, University of Alberta, Canada, E-mail: firstname.lastname@example.org.